Pulmonary Valve Atresia with Intact Ventricular Septum.
نویسنده
چکیده
A case of pulmonary valve atresia with intact ventricular septum' with long survival in the absence of a patent ductus arteriosus, is presented. The patient, alive at 21 years of age, has the anterior descending branch of the left coronary artery originating from the pulmonary artery. Thus, the pulmonary blood supply is obtained from the right coronary artery via intercoronary anastomoses. No similar case has been reported previously.
منابع مشابه
[Pulmonary atresia with intact ventricular septum associated with severe aortic stenosis].
Pulmonary atresia with intact ventricular septum is the complete obstruction of the right ventricular outflow tract due to pulmonary valve atresia in the absence of ventricular septal defect. Pulmonary flow is dependent on the ductus arteriosus. Other morphological anomalies are also present. Aortic stenosis in association with pulmonary atresia with intact ventricular septum is extremely infre...
متن کاملEchocardiographic assessment of neonates with pulmonary atresia and intact ventricular septum.
In this prospective study, 27 consecutive neonates suspected to be suffering from pulmonary atresia and intact ventricular septum underwent detailed two-dimensional echocardiographic examination before cardiac catheterization. Of the 27 neonates 25 had pulmonary atresia and intact ventricular septum and the remaining 2 had "functional pulmonary atresia" secondary to severe Ebstein's anomaly of ...
متن کاملPrenatal Diagnosis of Pulmonary Atresia with Intact Ventricular Septum
Hypoplasia of the right ventricle is uncommon as an isolated entity. It may result from tricuspid atresia, but is most commonly secondary to pulmonary atresia with intact ventricular septum. Pulmonary atresia with intact ventricular septum is rare, accounting for 1-3% of cases of congenital heart disease. It occurs in 0.1 to 0.4 in 10,000 live births. Pulmonary atresia with intact ventricular s...
متن کاملNew percutaneous techniques for perforating the pulmonary valve in pulmonary atresia with intact ventricular septum.
We report new percutaneous techniques for perforating the pulmonary valve in pulmonary atresia with intact ventricular septum, in 3 newborns who had this birth defect. There was mild to moderate hypoplastic right ventricle, a patent infundibulum, and no coronary-cavitary communications. We succeeded in all cases, and no complications related to the procedure occurred. The new coaxial radiofrequ...
متن کاملPulmonary atresia, "intact ventricular septum", and aortopulmonary collateral arteries.
In muscular pulmonary atresia, major aortopulmonary collateral arteries are characteristic of pulmonary atresia with ventricular septal defect and are rarely seen in pulmonary atresia with intact ventricular septum. Two unusual cases of muscular pulmonary atresia are reported, one with an intact septum and one with a perimembranous ventricular septal defect, closed in utero by aneurysmal tricus...
متن کاملPulmonary atresia with intact ventricular septum.
It is important to employ a strategy for pulmonary atresia with intact ventricular septum (PAIVS) in collaboration with cardiology and cardiac surgery. We established our policy of treatment based on the right ventricular end diastolic volume. Sinusoidal communication should be carefully considered. Prognosis was poor in case of interruption of coronary arteries. Although catheter intervention ...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
عنوان ژورنال:
- Cardiovascular diseases
دوره 2 2 شماره
صفحات -
تاریخ انتشار 1975